|EWA SZYGUŁA-KOTALA, MAGDALENA SĄDA-CIEŚLAR, ZOFIA BUSZMAN|
Hyper-IgE syndrome (Job syndrome, hyperIgE recurrent infection syndrome), a rare imunodeficiency, is characterized by recurrent skin and pulmonary abscesses, pneumonia with formation of pneumatoceles, recurrent eczematoid rashes, typical constitutional traits, as well as extremely high serum IgE levels. A case of a 2,5 year old boy with a Job syndrome and with the symptoms of eczematoid rashes, pneumonia and staphylococcal sepsis has been reported.
keywords: zespół hiper-IgE, hiper-IgE syndrome
pages: from 109 to 112
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